Björn Kowalewski
PEVZ-ID
9 Publikationen
-
2021 | Zeitschriftenaufsatz | E-Veröff. vor dem Druck | PUB-ID: 2956816B. Kowalewski, H. Lange, S. Galle, T. Dierks, T. Lübke, and M. Damme, “Decoding the consecutive lysosomal degradation of 3-O-sulfate containing heparan sulfate by Arylsulfatase G (ARSG)”, Biochemical Journal, 2021.PUB | DOI | WoS | PubMed | Europe PMC
-
2018 | Zeitschriftenaufsatz | Veröffentlicht | PUB-ID: 2931507S. Khateb, B. Kowalewski, N. Bedoni, M. Damme, N. Pollack, A. Saada, A. Obolensky, T. Ben-Yosef, M. Gross, T. Dierks, et al., “A homozygous founder missense variant in arylsulfatase G abolishes its enzymatic activity causing atypical Usher syndrome in humans”, GENETICS IN MEDICINE, 2018, 20, 1004-1012.PUB | DOI | WoS | PubMed | Europe PMC
-
-
2015 | Zeitschriftenaufsatz | Veröffentlicht | PUB-ID: 2709463B. Kowalewski, P. Heimann, T. Ortkras, R. Lüllmann-Rauch, T. Sawada, S. U. Walkley, T. Dierks, and M. Damme, “Ataxia is the major neuropathological finding in Arylsulfatase G deficient mice: Similarities and dissimilarities to Sanfilippo disease (Mucopolysaccharidosis type III)”, Human Molecular Genetics, 2015, 24, 1856-1868.PUB | DOI | WoS | PubMed | Europe PMC
-
2014 | Zeitschriftenaufsatz | Veröffentlicht | PUB-ID: 2690696J. Poppe, E. Warkentin, U. Demmer, B. Kowalewski, T. Dierks, K. Schneider, and U. Ermler, “Structural diversity of polyoxomolybdate clusters along the three-fold axis of the molybdenum storage protein”, Journal of Inorganic Biochemistry, 2014, 138, 122-128.PUB | DOI | WoS | PubMed | Europe PMC
-
2014 | Zeitschriftenaufsatz | Veröffentlicht | PUB-ID: 2699273B. Kowalewski, T. Lübke, K. Kollmann, T. Braulke, T. Reinheckel, T. Dierks, and M. Damme, “Molecular Characterization of Arylsulfatase G: EXPRESSION, PROCESSING, GLYCOSYLATION, TRANSPORT, AND ACTIVITY”, The Journal of biological chemistry, 2014, 289, 27992-28005.PUB | DOI | WoS | PubMed | Europe PMC
-
2013 | Zeitschriftenaufsatz | Veröffentlicht | PUB-ID: 2607389M. Yoo, M. Khaled, K. M. Gibbs, J. Kim, B. Kowalewski, T. Dierks, and M. Schachner, “Arylsulfatase B Improves Locomotor Function after Mouse Spinal Cord Injury”, Plos One, 2013, 8, : e57415.PUB | DOI | WoS | PubMed | Europe PMC
-
2012 | Zeitschriftenaufsatz | Veröffentlicht | PUB-ID: 2517966B. Kowalewski, J. Poppe, U. Demmer, E. Warkentin, T. Dierks, U. Ermler, and K. Schneider, “Nature's Polyoxometalate Chemistry: X-ray Structure of the Mo Storage Protein Loaded with Discrete Polynuclear Mo-O Clusters”, Journal of the American Chemical Society, 2012, 134, 9768-9774.PUB | DOI | WoS | PubMed | Europe PMC
-
2012 | Zeitschriftenaufsatz | Veröffentlicht | PUB-ID: 2494022B. Kowalewski, W. C. Lamanna, R. Lawrence, M. Damme, M. Padva, S. Stroobants, I. Kalus, M. - A. Frese, T. Lübke, R. Lüllmann-Rauch, et al., “Arylsulfatase G Inactivation Causes Loss of Heparan Sulfate 3-O-Sulfatase Activity and Mucopolysaccharidosis in Mice”, Proc. Natl. Acad. Sci. USA, 2012, 109, 10310-10315.PUB | DOI | WoS | PubMed | Europe PMC