PUB - Publikationen an der Universität Bielefeld

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• [14]
  

  2016 | Zeitschriftenaufsatz | Veröffentlicht | PUB-ID: 2904124

  Kruszewski, K., Luellmann-Rauch, R., Dierks, T., Bartsch, U., Damme, M.: Degeneration of Photoreceptor Cells in Arylsulfatase G-Deficient Mice. INVESTIGATIVE OPHTHALMOLOGY & VISUAL SCIENCE. 57, 1120-1131 (2016).

  PUB | DOI | WoS | PubMed | Europe PMC
   
• [13]
  

  2016 | Zeitschriftenaufsatz | Veröffentlicht | PUB-ID: 2905616

  Wolf, H., Damme, M., Stroobants, S., D'Hooge, R., Beck, H.C., Hermans-Borgmeyer, I., Lüllmann-Rauch, R., Dierks, T., Lübke, T.: A mouse model for fucosidosis recapitulates storage pathology and neurological features of the milder form of the human disease. Disease Models & Mechanisms. 9, 1015-1028 (2016).

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• [12]
  

  2015 | Zeitschriftenaufsatz | Veröffentlicht | PUB-ID: 2709463

  Kowalewski, B., Heimann, P., Ortkras, T., Lüllmann-Rauch, R., Sawada, T., Walkley, S.U., Dierks, T., Damme, M.: Ataxia is the major neuropathological finding in Arylsulfatase G deficient mice: Similarities and dissimilarities to Sanfilippo disease (Mucopolysaccharidosis type III). Human Molecular Genetics. 24, 1856-1868 (2015).

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• [11]
  

  2014 | Zeitschriftenaufsatz | Veröffentlicht | PUB-ID: 2658538

  Kong, X.Y., Nesset, C.K., Damme, M., Loeberg, E.-M., Lübke, T., Maehlen, J., Andersson, K.B., Roos, N., Thoresen, G.H., Rustan, A.C., Kase, E.T., Eskild, W.: Loss of lysosomal membrane protein NCU-G1 in mice results in spontaneous liver fibrosis with accumulation of lipofuscin and iron in Kupffer cells. Disease Models & Mechanisms. 7, 351-362 (2014).

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• [10]
  

  2012 | Zeitschriftenaufsatz | Veröffentlicht | PUB-ID: 2484642

  Thelen, M., Damme, M., Schweizer, M., Hagel, C., Wong, A., Cooper, J.D., Braulke, T., Galliciotti, G.: Disruption of the Autophagy-Lysosome Pathway is Involved in Neuropathology of the nclf Mouse Model of Neuronal Ceroid Lipofuscinosis. PLOS ONE. 7, : e35493 (2012).

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• [9]
  

  2012 | Zeitschriftenaufsatz | Veröffentlicht | PUB-ID: 2471754

  Makrypidi, G., Damme, M., Müller-Loennies, S., Trusch, M., Schmidt, B., Schlüter, H., Heeren, J., Lübke, T., Saftig, P., Braulke, T.: Mannose 6 dephosphorylation of lysosomal proteins mediated by Acid phosphatases acp2 and acp5. Molecular and cellular biology. 32, 774-782 (2012).

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• [8]
  

  2012 | Zeitschriftenaufsatz | Veröffentlicht | PUB-ID: 2529586

  Kollmann, K., Damme, M., Markmann, S., Morelle, W., Schweizer, M., Hermans-Borgmeyer, I., Rochert, A.K., Pohl, S., Lübke, T., Michalski, J.-C., Kakela, R., Walkley, S.U., Braulke, T.: Lysosomal dysfunction causes neurodegeneration in mucolipidosis II 'knock-in' mice. Brain. 135, 2661-2675 (2012).

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• [7]
  

  2012 | Zeitschriftenaufsatz | Veröffentlicht | PUB-ID: 2494022

  Kowalewski, B., Lamanna, W.C., Lawrence, R., Damme, M., Padva, M., Stroobants, S., Kalus, I., Frese, M.-A., Lübke, T., Lüllmann-Rauch, R., D'Hooge, R., Esko, J.D., Dierks, T.: Arylsulfatase G Inactivation Causes Loss of Heparan Sulfate 3-O-Sulfatase Activity and Mucopolysaccharidosis in Mice. Proc. Natl. Acad. Sci. USA. 109, 10310-10315 (2012).

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• [6]
  

  2011 | Zeitschriftenaufsatz | Veröffentlicht | PUB-ID: 1940515

  Damme, M., Stroobants, S., Walkley, S.U., Lüllmann-Rauch, R., D'Hooge, R., Fogh, J., Saftig, P., Lübke, T., Blanz, J.: Cerebellar alterations and gait defects as therapeutic outcome measures for enzyme replacement therapy in alpha-mannosidosis. Journal of Neuropathology & Experimental Neurology. 70, 83-94 (2011).

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• [5]
  

  2011 | Zeitschriftenaufsatz | Veröffentlicht | PUB-ID: 2352585

  Savalas, L.R., Gasnier, B., Damme, M., Lübke, T., Wrocklage, C., Debacker, C., Jezeqou, A., Reinheckel, T., Hasilik, A., Saftig, P., Schröder, B.: Disrupted in renal carcinoma 2 (DIRC2), a novel transporter of the lysosomal membrane, is proteolytically processed by cathepsin L. Biochemical Journal. 436, 113-121 (2011).

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• [4]
  

  2010 | Zeitschriftenaufsatz | Veröffentlicht | PUB-ID: 1902203

  Damme, M., Morelle, W., Schmidt, B., Andersson, C., Fogh, J., Michalski, J.-C., Lübke, T.: Impaired lysosomal trimming of N-linked oligosaccharides leads to hyperglycosylation of native lysosomal proteins in mice with alpha-mannosidosis. Molecular and Cellular Biology. 30, 273-283 (2010).

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• [3]
  

  2009 | Dissertation | PUB-ID: 2352701

  Damme, M.: Zellbiologische Untersuchung α-Mannosidase-defizienter und Enzym-behandelter Mäuse. (2009).

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• [2]
  

  2009 | Zeitschriftenaufsatz | Veröffentlicht | PUB-ID: 1902143

  Schieweck, O., Damme, M., Schröder, B., Hasilik, A., Schmidt, B., Lübke, T.: NCU-G1 is a highly glycosylated integral membrane protein of the lysosome. Biochemical Journal. 422, 83-90 (2009).

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• [1]
  

  2009 | Zeitschriftenaufsatz | Veröffentlicht | PUB-ID: 1940533

  Kollmann, K., Damme, M., Deuschl, F., Kahle, J., D'Hooge, R., Lüllmann-Rauch, R., Lübke, T.: Molecular characterization and gene disruption of mouse lysosomal putative serine carboxypeptidase 1. Febs Journal. 276, 1356-1369 (2009).

  PUB | DOI | WoS | PubMed | Europe PMC