PUB - Publikationen an der Universität Bielefeld

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• [14]
  

  2016 | Zeitschriftenaufsatz | Veröffentlicht | PUB-ID: 2904124

  Kruszewski, K., Luellmann-Rauch, R., Dierks, T., Bartsch, U., & Damme, M. (2016). Degeneration of Photoreceptor Cells in Arylsulfatase G-Deficient Mice. INVESTIGATIVE OPHTHALMOLOGY & VISUAL SCIENCE, 57(3), 1120-1131. doi:10.1167/iovs.15-17645

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• [13]
  

  2016 | Zeitschriftenaufsatz | Veröffentlicht | PUB-ID: 2905616

  Wolf, H., Damme, M., Stroobants, S., D'Hooge, R., Beck, H. C., Hermans-Borgmeyer, I., Lüllmann-Rauch, R., et al. (2016). A mouse model for fucosidosis recapitulates storage pathology and neurological features of the milder form of the human disease. Disease Models & Mechanisms, 9(9), 1015-1028. doi:10.1242/dmm.025122

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• [12]
  

  2015 | Zeitschriftenaufsatz | Veröffentlicht | PUB-ID: 2709463

  Kowalewski, B., Heimann, P., Ortkras, T., Lüllmann-Rauch, R., Sawada, T., Walkley, S. U., Dierks, T., et al. (2015). Ataxia is the major neuropathological finding in Arylsulfatase G deficient mice: Similarities and dissimilarities to Sanfilippo disease (Mucopolysaccharidosis type III). Human Molecular Genetics, 24(7), 1856-1868. doi:10.1093/hmg/ddu603

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• [11]
  

  2014 | Zeitschriftenaufsatz | Veröffentlicht | PUB-ID: 2658538

  Kong, X. Y., Nesset, C. K., Damme, M., Loeberg, E. - M., Lübke, T., Maehlen, J., Andersson, K. B., et al. (2014). Loss of lysosomal membrane protein NCU-G1 in mice results in spontaneous liver fibrosis with accumulation of lipofuscin and iron in Kupffer cells. Disease Models & Mechanisms, 7(3), 351-362. doi:10.1242/dmm.014050

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• [10]
  

  2012 | Zeitschriftenaufsatz | Veröffentlicht | PUB-ID: 2484642

  Thelen, M., Damme, M., Schweizer, M., Hagel, C., Wong, A., Cooper, J. D., Braulke, T., et al. (2012). Disruption of the Autophagy-Lysosome Pathway is Involved in Neuropathology of the nclf Mouse Model of Neuronal Ceroid Lipofuscinosis. PLOS ONE, 7(4), e35493. doi:10.1371/journal.pone.0035493

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• [9]
  

  2012 | Zeitschriftenaufsatz | Veröffentlicht | PUB-ID: 2471754

  Makrypidi, G., Damme, M., Müller-Loennies, S., Trusch, M., Schmidt, B., Schlüter, H., Heeren, J., et al. (2012). Mannose 6 dephosphorylation of lysosomal proteins mediated by Acid phosphatases acp2 and acp5. Molecular and cellular biology, 32(4), 774-782. doi:10.1128/MCB.06195-11

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• [8]
  

  2012 | Zeitschriftenaufsatz | Veröffentlicht | PUB-ID: 2529586

  Kollmann, K., Damme, M., Markmann, S., Morelle, W., Schweizer, M., Hermans-Borgmeyer, I., Rochert, A. K., et al. (2012). Lysosomal dysfunction causes neurodegeneration in mucolipidosis II 'knock-in' mice. Brain, 135(9), 2661-2675. doi:10.1093/brain/aws209

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• [7]
  

  2012 | Zeitschriftenaufsatz | Veröffentlicht | PUB-ID: 2494022

  Kowalewski, B., Lamanna, W. C., Lawrence, R., Damme, M., Padva, M., Stroobants, S., Kalus, I., et al. (2012). Arylsulfatase G Inactivation Causes Loss of Heparan Sulfate 3-O-Sulfatase Activity and Mucopolysaccharidosis in Mice. Proc. Natl. Acad. Sci. USA, 109(26), 10310-10315. doi:10.1073/pnas.1202071109

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• [6]
  

  2011 | Zeitschriftenaufsatz | Veröffentlicht | PUB-ID: 1940515

  Damme, M., Stroobants, S., Walkley, S. U., Lüllmann-Rauch, R., D'Hooge, R., Fogh, J., Saftig, P., et al. (2011). Cerebellar alterations and gait defects as therapeutic outcome measures for enzyme replacement therapy in alpha-mannosidosis. Journal of Neuropathology & Experimental Neurology, 70(1), 83-94. https://doi.org/10.1097/NEN.0b013e31820428fa

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• [5]
  

  2011 | Zeitschriftenaufsatz | Veröffentlicht | PUB-ID: 2352585

  Savalas, L. R., Gasnier, B., Damme, M., Lübke, T., Wrocklage, C., Debacker, C., Jezeqou, A., et al. (2011). Disrupted in renal carcinoma 2 (DIRC2), a novel transporter of the lysosomal membrane, is proteolytically processed by cathepsin L. Biochemical Journal, 436(1), 113-121. https://doi.org/10.1042/BJ20101672

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• [4]
  

  2010 | Zeitschriftenaufsatz | Veröffentlicht | PUB-ID: 1902203

  Damme, M., Morelle, W., Schmidt, B., Andersson, C., Fogh, J., Michalski, J. - C., & Lübke, T. (2010). Impaired lysosomal trimming of N-linked oligosaccharides leads to hyperglycosylation of native lysosomal proteins in mice with alpha-mannosidosis. Molecular and Cellular Biology, 30(1), 273-283. https://doi.org/10.1128/MCB.01143-09

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• [3]
  

  2009 | Dissertation | PUB-ID: 2352701

  Damme, M. (2009). Zellbiologische Untersuchung α-Mannosidase-defizienter und Enzym-behandelter Mäuse.

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• [2]
  

  2009 | Zeitschriftenaufsatz | Veröffentlicht | PUB-ID: 1902143

  Schieweck, O., Damme, M., Schröder, B., Hasilik, A., Schmidt, B., & Lübke, T. (2009). NCU-G1 is a highly glycosylated integral membrane protein of the lysosome. Biochemical Journal, 422(1), 83-90. https://doi.org/10.1042/BJ20090567

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• [1]
  

  2009 | Zeitschriftenaufsatz | Veröffentlicht | PUB-ID: 1940533

  Kollmann, K., Damme, M., Deuschl, F., Kahle, J., D'Hooge, R., Lüllmann-Rauch, R., & Lübke, T. (2009). Molecular characterization and gene disruption of mouse lysosomal putative serine carboxypeptidase 1. Febs Journal, 276(5), 1356-1369. https://doi.org/10.1111/j.1742-4658.2009.06877.x

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