PUB - Publikationen an der Universität Bielefeld

Alle markieren

• [14]
  

  2016 | Zeitschriftenaufsatz | Veröffentlicht | PUB-ID: 2904124

  Kruszewski K, Luellmann-Rauch R, Dierks T, Bartsch U, Damme M. Degeneration of Photoreceptor Cells in Arylsulfatase G-Deficient Mice. INVESTIGATIVE OPHTHALMOLOGY & VISUAL SCIENCE. 2016;57(3):1120-1131.

  PUB | DOI | WoS | PubMed | Europe PMC
   
• [13]
  

  2016 | Zeitschriftenaufsatz | Veröffentlicht | PUB-ID: 2905616

  Wolf H, Damme M, Stroobants S, et al. A mouse model for fucosidosis recapitulates storage pathology and neurological features of the milder form of the human disease. Disease Models & Mechanisms. 2016;9(9):1015-1028.

  PUB | PDF | DOI | WoS | PubMed | Europe PMC
   
• [12]
  

  2015 | Zeitschriftenaufsatz | Veröffentlicht | PUB-ID: 2709463

  Kowalewski B, Heimann P, Ortkras T, et al. Ataxia is the major neuropathological finding in Arylsulfatase G deficient mice: Similarities and dissimilarities to Sanfilippo disease (Mucopolysaccharidosis type III). Human Molecular Genetics. 2015;24(7):1856-1868.

  PUB | DOI | WoS | PubMed | Europe PMC
   
• [11]
  

  2014 | Zeitschriftenaufsatz | Veröffentlicht | PUB-ID: 2658538

  Kong XY, Nesset CK, Damme M, et al. Loss of lysosomal membrane protein NCU-G1 in mice results in spontaneous liver fibrosis with accumulation of lipofuscin and iron in Kupffer cells. Disease Models & Mechanisms. 2014;7(3):351-362.

  PUB | PDF | DOI | WoS | PubMed | Europe PMC
   
• [10]
  

  2012 | Zeitschriftenaufsatz | Veröffentlicht | PUB-ID: 2484642

  Thelen M, Damme M, Schweizer M, et al. Disruption of the Autophagy-Lysosome Pathway is Involved in Neuropathology of the nclf Mouse Model of Neuronal Ceroid Lipofuscinosis. PLOS ONE. 2012;7(4): e35493.

  PUB | DOI | WoS | PubMed | Europe PMC
   
• [9]
  

  2012 | Zeitschriftenaufsatz | Veröffentlicht | PUB-ID: 2471754

  Makrypidi G, Damme M, Müller-Loennies S, et al. Mannose 6 dephosphorylation of lysosomal proteins mediated by Acid phosphatases acp2 and acp5. Molecular and cellular biology. 2012;32(4):774-782.

  PUB | DOI | WoS | PubMed | Europe PMC
   
• [8]
  

  2012 | Zeitschriftenaufsatz | Veröffentlicht | PUB-ID: 2529586

  Kollmann K, Damme M, Markmann S, et al. Lysosomal dysfunction causes neurodegeneration in mucolipidosis II 'knock-in' mice. Brain. 2012;135(9):2661-2675.

  PUB | DOI | WoS | PubMed | Europe PMC
   
• [7]
  

  2012 | Zeitschriftenaufsatz | Veröffentlicht | PUB-ID: 2494022

  Kowalewski B, Lamanna WC, Lawrence R, et al. Arylsulfatase G Inactivation Causes Loss of Heparan Sulfate 3-O-Sulfatase Activity and Mucopolysaccharidosis in Mice. Proc. Natl. Acad. Sci. USA. 2012;109(26):10310-10315.

  PUB | DOI | WoS | PubMed | Europe PMC
   
• [6]
  

  2011 | Zeitschriftenaufsatz | Veröffentlicht | PUB-ID: 1940515

  Damme M, Stroobants S, Walkley SU, et al. Cerebellar alterations and gait defects as therapeutic outcome measures for enzyme replacement therapy in alpha-mannosidosis. Journal of Neuropathology & Experimental Neurology. 2011;70(1):83-94.

  PUB | DOI | WoS | PubMed | Europe PMC
   
• [5]
  

  2011 | Zeitschriftenaufsatz | Veröffentlicht | PUB-ID: 2352585

  Savalas LR, Gasnier B, Damme M, et al. Disrupted in renal carcinoma 2 (DIRC2), a novel transporter of the lysosomal membrane, is proteolytically processed by cathepsin L. Biochemical Journal. 2011;436(1):113-121.

  PUB | DOI | WoS | PubMed | Europe PMC
   
• [4]
  

  2010 | Zeitschriftenaufsatz | Veröffentlicht | PUB-ID: 1902203

  Damme M, Morelle W, Schmidt B, et al. Impaired lysosomal trimming of N-linked oligosaccharides leads to hyperglycosylation of native lysosomal proteins in mice with alpha-mannosidosis. Molecular and Cellular Biology. 2010;30(1):273-283.

  PUB | DOI | WoS | PubMed | Europe PMC
   
• [3]
  

  2009 | Dissertation | PUB-ID: 2352701

  Damme M. Zellbiologische Untersuchung α-Mannosidase-defizienter und Enzym-behandelter Mäuse.; 2009.

  PUB | Download (ext.)
   
• [2]
  

  2009 | Zeitschriftenaufsatz | Veröffentlicht | PUB-ID: 1902143

  Schieweck O, Damme M, Schröder B, Hasilik A, Schmidt B, Lübke T. NCU-G1 is a highly glycosylated integral membrane protein of the lysosome. Biochemical Journal. 2009;422(1):83-90.

  PUB | DOI | WoS | PubMed | Europe PMC
   
• [1]
  

  2009 | Zeitschriftenaufsatz | Veröffentlicht | PUB-ID: 1940533

  Kollmann K, Damme M, Deuschl F, et al. Molecular characterization and gene disruption of mouse lysosomal putative serine carboxypeptidase 1. Febs Journal. 2009;276(5):1356-1369.

  PUB | DOI | WoS | PubMed | Europe PMC